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Some of the Cummins' School medalists.
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Some of the Cummins' School medalists.
Maggie Priole, 10, from Glenside, was ranked first in north America for her age in the treble jig round, earning two perfect 100’s from 2 of the three judges at the North American Irish Dance Championship, held July 3-7, in Chicago. Maggie, who is a student at the Cummins School in Philadelphia, placed fourth overall in North America . She attends 3 three-hour classes a week, plus 2-3 private lessons a week, and has a private strength-training session geared towards Irish dancers each week, proving that winning takes work. Congrats, Maggie!
Other Cummins School dancers also came back with medals. Mairin McDonnell age 10 from Jenkintown came in 25th. Mairin also competed in February at the all Ireland champs in Dublin. Ellie Lynch, 9, from Oreland was franked in 35th place. Katie Donnelly, 16 from, Manayunk came in 56th place. This is the first year Katie qualified for North American competition. She also received a medal at the All Ireland’s in February.
The Cummins School is located at the Irish Center in Mt. Airy.
Editors’ note: How did your dancers do? Email us with the information at denise.foley@comcast.net and we’ll let everyone know. Pictures welcome!
Monday June 25. The first piece of Philadelphia GAA . 2012 Ladies’ silverware has been lifted by the resilient Notre Dames on Sunday, June 24th. The Mairéad Farrell Memorial League Cup is in the grasp of the Notre Dames. After a one-year hiatus, they are back with a bit of vengeance. They were 2010 North American Intermediate Champions, and North American Junior ‘A’ Champions in a previous year.
Game One took place Sunday, June 17, with a result of 04-11 to 02-11 in favor of the Dames, on the back of three onion bag-busting goals in the second half alone. They sprayed first-time, diagonal balls straight into the half-forward Line with great success.
The Mairéad Farrells could only get the engine to tick over rather than putting it into their usual, maximum overdrive. The Farrells have experienced great success in their three years of existence, going to the Senior North American Semi-Finals in year one, and winning back-to-back North American Senior Titles in 2010 and 2011.
Both clubs have great stewards in between the uprights, minding the goalmouth, and both young women are American-born: Katie Kavanagh Mills for the Dames and Desiree DaBaldo for the Farrells. Mills made two saves from point blank range, which kept them in Game One in the first half. DaBaldo was exceptional in punching a rocket over the bar, conceding a point; and stopping three additional goal opportunities with her cat-like reflexes.
Game Two on Sunday, June 24, was a walkover, as the Mairéad Farrells elected to forfeit the fixture. Reports from the Farrell’s camp was that they have some girls who are carrying injuries, and another few who had prior engagements at the Beach Blast Soccer Tournament in the Wildwoods.
Philadelphia GAA spectators should be in for a treat this summer with Ladies’ football action. Manager Darren Hart has discovered the right formula to achieve two previous North Americans. Previous management got them in the right zip code but had trouble locating the Address. Will the Dames farther ascend the escalator of success, and advance to the Ladies North American Senior Finals? Trish Monaghan, Maureen Ennis, and Company certainly appear to have found most of the Ingredients for a winning recipe.
However, even with the weather well up into the high 90s and flirting with triple digits, Angela Mohan, Ciara Moore and Company have the gloves on, not willing to show their hands. They have a knack for pulling the trump cards out at the perfect time. Will the Farrells let the clutch out and motor on rampantly as they have in the past? Can the possible 3-in-a-row provide the grease needed for what opponents have referred to as a machine? When the curtain on the ladies championship is raised, there will be plenty of sore heads and lost voices before its all over, and lucky for us spectators, it hasn’t even begun.
With a tally of four North American Titles between these two clubs in the last three years, clearly Philadelphia is going to be the toll booth to the 2012 North American Senior Ladies Championship. Guess what? Neither one of these clubs is accepting E-Z Pass.
By Peter McDermott
By Peter McDermott
Sunday, June 24. The Saint Pat's Club lifted the second piece of available silverware in Philadelphia men's Gaelic football–the Jim Harvey Memorial League Cup–by a scoreline of 3-12 to 0-11. Jim Harvey was from Donegal Town, and was a great ambassador of the games here in Philadelphia. When his name is mentioned, it is with reference and respect by all that knew him.
Saint Pat's led at the half over the Young Irelands by a score of 1-05 to 0-07, the minimum. The Young Irelands weren't getting a ton of scoring opportunities, but when they were available, they were slotting them over. With just 20 minutes gone, the Young Irelands were reduced to 12, after Referee Joe McGinn displayed the red card. Young Irelands put six points on the board before registering their first wide of the day. They would finish the half with just two wides. Scores came off of Declan Gormley, Patrick O'Hara, Martin Curran, and Sean McTernan.
Saint Pat's was struggling to convert their fluid play into scores during that first half, kicking five wides and lobbing two gifts straight into the keeper, Shane Callaghan's hands. It was near the short whistle with 27 minutes gone that Stevie Robinson sent the size five into the back of the net, putting just a point between them. Scores came off of Ciaran Porter, Stevie Robinson, and Lee Moore.
The second half resumed and both clubs couldn't find the target as shots were sailing just outside the posts. Both clubs made adjustments and the shooting improved. Young Irelands kept matters close till the 45-minute mark, but signs of fatigue were starting to show. The man advantage was starting to open the cracks in the Young Ireland's façade. The loss of workhorse, Adrian Mark, to injury only compounded their problems.
Midfielder Lesley Stevenson was thrown onto the top of the 20-meter line to create havoc for the Saint Pat's backline. The demand was there but the supply of ball was scarce. Instead of dropping balls into the Big Man via express airmail, they were going in 3-day ground parcel and to the wrong address. Then, they tried forcing balls into closed corridors that should have been popped over the bar.
High tide was coming, and the flooding started. Liam O'Donnell got loose inside the large parallelogram, but was denied by Shane Callaghan. Moments later, Lee Moore slipped inside his Defender, but his shot was also turned away for a 45 meter kick. The 45 was beautifully converted by Matt Crossan, with plenty to spare. That point was the beginning of the end.
The next time Liam O'Donnell got away from his marker, his shot was stopped again; very uncharacteristic based on past performances from “OD.” Shortly thereafter, Lee Moore pointed from play with his back to the uprights. American- born Conor Canavan, never left his side; but whenever Moore did find the space, he usually converted. The next ball came into Lee Moore and with a bit of dummying and sidestepping he was all alone with only Keeper Callaghan to beat. Callaghan had no option but to pull him down, and the ensuing penalty was converted by Moore. Another fine 45 from Matt Crossan, and Liam O'Donnell wasn't to be denied again, as his third time was the charm for a goal. Scores for Saint Pat's came from John Docherty, Ciaran Greene, Lee Moore, Liam O'Donnell, Stevie Robinson, and Matt Crossan.
Up next Sunday, is the Kevin McCartan Memorial Tournament Cup, which will be a Seven-a-Side Format. Most would put the Favorites Tag on the Saint Pat's Club, but within days the landscape of these teams could and will change.
Just a fortnight away from the start of the championship, and over 3 weeks to acquire the outside help before the July 20 deadline; those who have help coming will be welcoming it with open arms.
Predictions? I'll respectfully decline. We all know Saint Pat's will most likely be adding a few more, including a
new keeper (no disrespect intended, Mr. Cannon). The Kevin Barrys have a couple landed and it's rumored that there's more coming shortly. Young Irelands must add to their panel, after this day’s final.
Saint Pat's have scored 11 goals in the last two games. Any opposing clubs ringing for players, you may want to try for a couple of backs.
Monday, June 25 Those familiar colors have been making an Appearance at the Gaelic Field adjacent to the shuttered Cardinal Dougherty High School during the last four (4) weekends. The Green & Gold of Tir Chonaill, repackaged as the Saint Patrick's Gaelic Football Club.
Over the past couple years, the club redirected their focus on a rebuilding process centered around a youth program, which was composed of mostly American-born players. However, the calendar has changed, and so has the face of this club. Their selection of sanction players and the return of other players are making a lot of noise within the Philadelphia GAA.
On Sunday, June 10, their gifted American-born players lifted the Bill Drake Memorial League Cup, with a win over the Philadelphia Éire Óg boys. I'm sure that piece of hardware became well acquainted with a majority of the finest spirits in Jack Quinn's Lamplighter Tavern.
Then on Sunday, June 24, in the Jim Harvey Memorial Cup League fixture, Saint Pat's pummeled a depleted Kevin Barrys team by a score of 8-15 to 1-05; to advance to the final.
Sunday July 8 Since the Jim Harvey Cup Final, Saint Patrick's have added a big man between the posts to protect the house, Ryan Monteith. Young Ireland's picked up a cornerback in Niall McQuillan, a wing halfback in Caolan Haughey, and a dangerous forward in Patrick Quinn. Would it be enough?
Young Ireland's jumped out of the gate with some good ball work, trying to pump balls into Patrick Quinn, Patrick O'Hara, and Luke Coyle. David Doyle, Ciaran Greene, Paul Butcher, and Patrick Kennedy did well for Saint Patrick's in cutting off the incoming supply. Quinn had trouble turning his defender. Unable to get inside, he slotted over a marvelous point from the most acute of angles; well inside the 20-meter line and over near the sideline.
Monteith's kickouts were massive, falling out of the sky, when needed; or sent as long, sharp passes when midfield was congested. Quinn looked like he was going to completely torture Saint Patrick's when he hammered the ball, low and hard, on Monteith's short side for a goal. Saint Patrick's management switched a couple markers in front of Quinn, rather than suffocating him, and the moves worked. Declan Gormley and Patrick O'Hara also added nice scores for the Young Ireland's. Scores for Saint Patrick's came off Stevie Robinson, Liam O'Donnell, Lee Moore and Ciaran Porter. Two-point advantage to the Young Ireland's.
Half-Time:
Young Ireland's 1-05 to Saint Patrick's 0-06
The second half started under the assumption that the Saint Patrick's squad must have received an earful at the half, as they seemed to sharpen up between the 45s. Saint Patrick's began to attack from the halfback line of Doyle, Greene and John Doherty, who were fed from balls cleaned up by the two cornerbacks, Butcher and Kennedy. Lee Moore, Robinson, and O'Donnell took some good points for Saint Patrick's. The highlight reel of the game came when Lee Moore served up a gem straight onto the laces of Robinson, which he volleyed one-time into the back of the net. The gift-wrapping was done by the Craigbane forward, leaving his Ballerin counterpart only to stick a bow on it. Young Ireland's managed another point, but couldn't get the equalizer. Tough loss for the Red and Black.
Full-Time:
Saint Patrick's • 3-10 to Young Ireland's • 1-12
Up Next in Division I Men's Football, Sunday, July 15: the Young Ireland's hope to bounce back against the Kevin Barry's. The Barrys have been sitting and watching patiently, since June 17.. They have added Stephen Slater, Paul Johnston, Stephen Shannon, David McGarrity, Francis McCrudden, Conor McClelland, Patrick Fox, Conall Duffy, Ger O'Sullivan, and Dean McNally, thus far. Paperwork is rumored in the pipeline for Stefan McKenna, and Peter Mallon.
Young Ireland's will add at least Kevin Davey to the lineup.
By Peter McDermott
Sunday, June 24. The Saint Pat's Club lifted the second piece of available silverware in Philadelphia men's Gaelic football–the Jim Harvey Memorial League Cup–by a scoreline of 3-12 to 0-11. Jim Harvey was from Donegal Town, and was a great ambassador of the games here in Philadelphia. When his name is mentioned, it is with reference and respect by all that knew him.
Saint Pat's led at the half over the Young Irelands by a score of 1-05 to 0-07, the minimum. The Young Irelands weren't getting a ton of scoring opportunities, but when they were available, they were slotting them over. With just 20 minutes gone, the Young Irelands were reduced to 12, after Referee Joe McGinn displayed the red card. Young Irelands put six points on the board before registering their first wide of the day. They would finish the half with just two wides. Scores came off of Declan Gormley, Patrick O'Hara, Martin Curran, and Sean McTernan.
Saint Pat's was struggling to convert their fluid play into scores during that first half, kicking five wides and lobbing two gifts straight into the keeper, Shane Callaghan's hands. It was near the short whistle with 27 minutes gone that Stevie Robinson sent the size five into the back of the net, putting just a point between them. Scores came off of Ciaran Porter, Stevie Robinson, and Lee Moore.
The second half resumed and both clubs couldn't find the target as shots were sailing just outside the posts. Both clubs made adjustments and the shooting improved. Young Irelands kept matters close till the 45-minute mark, but signs of fatigue were starting to show. The man advantage was starting to open the cracks in the Young Ireland's façade. The loss of workhorse, Adrian Mark, to injury only compounded their problems.
Midfielder Lesley Stevenson was thrown onto the top of the 20-meter line to create havoc for the Saint Pat's backline. The demand was there but the supply of ball was scarce. Instead of dropping balls into the Big Man via express airmail, they were going in 3-day ground parcel and to the wrong address. Then, they tried forcing balls into closed corridors that should have been popped over the bar.
High tide was coming, and the flooding started. Liam O'Donnell got loose inside the large parallelogram, but was denied by Shane Callaghan. Moments later, Lee Moore slipped inside his Defender, but his shot was also turned away for a 45 meter kick. The 45 was beautifully converted by Matt Crossan, with plenty to spare. That point was the beginning of the end.
The next time Liam O'Donnell got away from his marker, his shot was stopped again; very uncharacteristic based on past performances from “OD.” Shortly thereafter, Lee Moore pointed from play with his back to the uprights. American- born Conor Canavan, never left his side; but whenever Moore did find the space, he usually converted. The next ball came into Lee Moore and with a bit of dummying and sidestepping he was all alone with only Keeper Callaghan to beat. Callaghan had no option but to pull him down, and the ensuing penalty was converted by Moore. Another fine 45 from Matt Crossan, and Liam O'Donnell wasn't to be denied again, as his third time was the charm for a goal. Scores for Saint Pat's came from John Docherty, Ciaran Greene, Lee Moore, Liam O'Donnell, Stevie Robinson, and Matt Crossan.
Up next Sunday, is the Kevin McCartan Memorial Tournament Cup, which will be a Seven-a-Side Format. Most would put the Favorites Tag on the Saint Pat's Club, but within days the landscape of these teams could and will change.
Just a fortnight away from the start of the championship, and over 3 weeks to acquire the outside help before the July 20 deadline; those who have help coming will be welcoming it with open arms.
Predictions? I'll respectfully decline. We all know Saint Pat's will most likely be adding a few more, including a
new keeper (no disrespect intended, Mr. Cannon). The Kevin Barrys have a couple landed and it's rumored that there's more coming shortly. Young Irelands must add to their panel, after this day’s final.
Saint Pat's have scored 11 goals in the last two games. Any opposing clubs ringing for players, you may want to try for a couple of backs.
Monday, June 25 Those familiar colors have been making an Appearance at the Gaelic Field adjacent to the shuttered Cardinal Dougherty High School during the last four (4) weekends. The Green & Gold of Tir Chonaill, repackaged as the Saint Patrick's Gaelic Football Club.
Over the past couple years, the club redirected their focus on a rebuilding process centered around a youth program, which was composed of mostly American-born players. However, the calendar has changed, and so has the face of this club. Their selection of sanction players and the return of other players are making a lot of noise within the Philadelphia GAA.
On Sunday, June 10, their gifted American-born players lifted the Bill Drake Memorial League Cup, with a win over the Philadelphia Éire Óg boys. I'm sure that piece of hardware became well acquainted with a majority of the finest spirits in Jack Quinn's Lamplighter Tavern.
Then on Sunday, June 24, in the Jim Harvey Memorial Cup League fixture, Saint Pat's pummeled a depleted Kevin Barrys team by a score of 8-15 to 1-05; to advance to the final.
Sunday July 8 Since the Jim Harvey Cup Final, Saint Patrick's have added a big man between the posts to protect the house, Ryan Monteith. Young Ireland's picked up a cornerback in Niall McQuillan, a wing halfback in Caolan Haughey, and a dangerous forward in Patrick Quinn. Would it be enough?
Young Ireland's jumped out of the gate with some good ball work, trying to pump balls into Patrick Quinn, Patrick O'Hara, and Luke Coyle. David Doyle, Ciaran Greene, Paul Butcher, and Patrick Kennedy did well for Saint Patrick's in cutting off the incoming supply. Quinn had trouble turning his defender. Unable to get inside, he slotted over a marvelous point from the most acute of angles; well inside the 20-meter line and over near the sideline.
Monteith's kickouts were massive, falling out of the sky, when needed; or sent as long, sharp passes when midfield was congested. Quinn looked like he was going to completely torture Saint Patrick's when he hammered the ball, low and hard, on Monteith's short side for a goal. Saint Patrick's management switched a couple markers in front of Quinn, rather than suffocating him, and the moves worked. Declan Gormley and Patrick O'Hara also added nice scores for the Young Ireland's. Scores for Saint Patrick's came off Stevie Robinson, Liam O'Donnell, Lee Moore and Ciaran Porter. Two-point advantage to the Young Ireland's.
Half-Time:
Young Ireland's 1-05 to Saint Patrick's 0-06
The second half started under the assumption that the Saint Patrick's squad must have received an earful at the half, as they seemed to sharpen up between the 45s. Saint Patrick's began to attack from the halfback line of Doyle, Greene and John Doherty, who were fed from balls cleaned up by the two cornerbacks, Butcher and Kennedy. Lee Moore, Robinson, and O'Donnell took some good points for Saint Patrick's. The highlight reel of the game came when Lee Moore served up a gem straight onto the laces of Robinson, which he volleyed one-time into the back of the net. The gift-wrapping was done by the Craigbane forward, leaving his Ballerin counterpart only to stick a bow on it. Young Ireland's managed another point, but couldn't get the equalizer. Tough loss for the Red and Black.
Full-Time:
Saint Patrick's • 3-10 to Young Ireland's • 1-12
Up Next in Division I Men's Football, Sunday, July 15: the Young Ireland's hope to bounce back against the Kevin Barry's. The Barrys have been sitting and watching patiently, since June 17.. They have added Stephen Slater, Paul Johnston, Stephen Shannon, David McGarrity, Francis McCrudden, Conor McClelland, Patrick Fox, Conall Duffy, Ger O'Sullivan, and Dean McNally, thus far. Paperwork is rumored in the pipeline for Stefan McKenna, and Peter Mallon.
Young Ireland's will add at least Kevin Davey to the lineup.
Who knew we had so many friends?
Last Saturday morning, we launched a website to raise funds for our CD project, “Ceili Drive: The Music of Irish Philadelphia.” The goal: $3,000. We figured it might take a few weeks to hit the $3,000 mark, and even then, we might not hit our goal.
How wrong we were–in a really good way.
As of midday Tuesday, we were just $830 short of our target, which was, all by itself, pretty amazing. We never thought we’d get so far, so fast. But we weren’t prepared for the incredible surprise that greeted us the morning of Independence Day, by which time we had officially crossed the $3,200 mark. All that was thanks to amazing generosity from many people, with a big assist—$500—from the great Delaware Valley band Blackthorn.
All told, 55 people or organizations contributed to our fund. Even more surprising: More money continued to flow in, even after we had ripped past the $3,000 mark. As of Friday midday, we’d raised $3,420.
With that, we can now very comfortably move on to production of our CD, which showcases Irish traditional music from many of the area’s finest players and singers, moving them to center stage—right where they belong. Our plan was to share the talents of mature veterans and young upstarts alike, and to draw attention to the role families play in upholding the tradition, and moving it forward. (Kudos to the the Boyces, Brennans, and McGillians, all of whom contribute tunes to the effort.) Of course, Irish music in Philadelphia probably wouldn’t be as rich and as vibrant as it is without the contributions of Irish natives who now make the Delaware valley their home. Their influence on the making of “Ceili Drive” is also significant.
That we are where we are now is actually pretty remarkable, given that we’d never done anything like a recording project before, and often had no idea what we were doing. (Thanks to our musicians for their patience, and for setting us straight when we needed it.)
Clearly, we had a lot to learn. Then again, maybe recording a CD really is just that challenging. Harper Ellen Tepper, in an email a few weeks ago, helped us put it all in perspective: “Recording projects, like home improvements and divorces, take longer than you think, cost more than estimated, make a big mess and are SO nice when they are over.”
Ain’t it the truth.
So, here is where we are.
We recorded six original tracks in Milkboy Studios. We have six additional tracks donated by musicians who have previously recorded on their own. Now we move on to final production. All of that is what the $3,000 is for.
There are some loose ends we need to tie up, but we expect to release “Ceili Drive” toward the end of the summer. (And, though we’ve mentioned it before, it bears mentioning again: Our gratitude to Facebook fan Pete McDermott for suggesting the clever name.)
Thank-you gifts should be mailed out to all of our donors at about the same time.
The ultimate thank-you, we hope, will be “Ceili Drive” itself. We’re onto something special here, and we can’t wait for you to hear it.
This weekend through August 26, you can see what Irish musicians do in their spare time. A show featuring the other talents of a group of fiddlers, guitarists, and singers opens on Friday, July 6, and runs through August 26 at the Water Elemental Crafts and Fine Art Gallery in Lansdale.
Tipperary singer and guitarist Pat Egan, for example, is a photographer. Ellen Tepper, who is usually wrapped around a harp, creates wondrous Celtic knot windows and other mixed media work. Harpist Irish Nevins, guitarist John Brennan and fiddler Bette Conway, who co-owns the gallery, create fine jewelry. They’re just a few of the musician-artists whose work will be on display. Bonus: Count on hearing some live music at the gallery at 319 W. Main Street in Lansdale.
Speaking of live music, you can see Timlin & Kane all over the place this week. After Friday night at the St. James Gate Pub at the Sands Casino in Bethlehem (Friday), they’ll be performing at JD McGillicuddy’s in Kirklyn on Saturday night and making an encore appearance at Catherine Rooney’s Irish Pub in Wilmington, DE, next Friday, July 13.
Another treat this week: Raymond and Mickey Coleman of Tyrone (and Philly and New York) will be performing together with fiddler Plunkett McGartland in a foot-stomping, hand-clapping show at the Plough and the Stars at 123 Chestnut Street in Philadelphia on Thursday, July 12. I haven’t heard the Colemans together live yet, but here’s a little taste. You can’t just drop in—they’re selling tickets and they’re going fast. Give the Plough and the Stars a call.
If you’re looking for a day trip with a Celtic flavor, next weekend is the 2012 Irish Festival in Annapolis, MD, featuring Scythian, Albannach, Barleyjuice, Screaming Orphans, Seamus Kennedy, The Rovers, Kilmaine Saints, Crossing Celtic, the Chesapeake Caledonian Pipes and Drums and many others. There will be visits from some of the animal ambassadors from Busch Gardens and pony rides and other treats for the kids. So, tear yourself away from the shore to go to another shore just a few hours south.
When Cathy Mitchell’s son, Harrison, was diagnosed with Tay-Sachs disease, she and her husband, Jeff, were devastated–and more than a little confused.
“I thought Tay Sachs was a Jewish disease,” says Cathy. The Mitchells, who live in Langhorne, then learned that this deadly inherited disease, which cripples and kills, is common among people of Irish descent. As many as 1 in 50 Irish Americans is a carrier.
Children can only inherit the disease when both parents carry the trait; with every pregnancy, a couple runs a 25 percent chance of having a child with Tay Sachs and a 50 percent chance of having one who is a carrier but doesn’t have the disease. Cathy and Jeff Mitchell are both carriers.
“I didn’t even know I was Irish,” said Jeff Mitchell, who, with his wife and another couple–Aaron and Kathryn Harney of Downingtown—manned an information booth on Tay Sachs at the recent Irish Festival on Penn’s Landing. Mitchell hadn’t been close to his father’s side of the family and only learned after Harrison was diagnosed that his grandfather was Irish.
Like other children with Tay-Sachs, Harrison seemed like a perfectly normal baby when he was born. But at six months, he began showing troubling symptoms. “Harrison didn’t sit up. His muscle tone was weak,” says Jeff, a shop foreman at a truck equipment company. “When you would pick him up he would fall over. He startled to loud noises. He rolled over once and then never rolled over again.”
When Harrison seemed to have trouble seeing toys in front of him, the Mitchells took him to their pediatrician who, says Jeff Mitchell, “kept pushing it off on the fact that Harrison was born a month early,” implying he was experiencing normal developmental delays. Eventually, the Mitchells took their baby to a pediatric opthamologist who saw a cherry-red spot on his retina, a physical marker of Tay-Sachs.
The disease is a particularly cruel one. New parents come home with an infant who appears to be healthy and normal, but is lacking an important enzyme, hexosaminidase (Hex-A), that helps clear out fatty protein and other substances from the tissues and nerve cells of the brain. That regular housecleaning allows the infant to develop vision, hearing, movement, and other vital functions. For a few months, the Tay-Sachs babies grow and develop as babies do—cooing, reaching for toys, smiling, laughing, turning over.
But as those proteins build up in the tissues and nerve cells, a relentless deterioration of physical and mental abilities begins. Children lose their sight and hearing. Their muscles atrophy and they become paralyzed. Eventually, they’re unable to swallow, and they develop seizures and dementia. Most children born with Tay-Sachs die by the time they’re five. “They just slowly fade away,” says Jeff.
In 2010, Harrison Mitchell died just shy of his sixth birthday.
Unfortunately, most doctors don’t encourage any but their Jewish patients—particularly Ashkenazi Jews–to be tested for Tay-Sachs. They also may not recognize the symptoms when they see them in children like Harrison. Like the Mitchells, Kathryn and Aaron Harney saw doctor after doctor before their son, Nathan, now 18 months old, was diagnosed—again, by a pediatric opthamologist. “A lot of doctors looked and us and said, ‘Well, you’re first-time parents. . . .,” says Kathryn Harney, Nathan slouching on her lap, his hazel eyes wandering, unfocused.
Like the Mitchells, they Harneys didn’t know that Tay-Sachs is common among the Irish. After they were tested, Aaron Harney learned that he carries a strain common among French Canadians. “I didn’t realize I had French Canadian ancestors,” he says. Tay-Sachs is even more common in French Canadians and Cajuns than in the Irish—an estimated 1 in 27 carry the trait, the same as Ashkenazi Jews. Nathan also has a rare form of Tay-Sachs that more often occurs in older children. “That gives us some hope that he might survive longer,” says Kathryn.
There’s no cure for Tay-Sachs, but it can be prevented with genetic screening. The National Tay-Sachs & Allied Diseases Association of the Delaware Valley offers free Tay-Sachs screening to anyone over the age of 18. Researchers at Einstein Medical Center’s Genetics Division in Philadelphia are now conducting a study to determine an accurate carrier rate for Tay-Sachs disease in the Irish and to identify the most common gene changes in this demographic. If you qualify for the research project (you must have at least three Irish grandparents), you will be screened for free and also get genetic counseling to explain your results and discuss your options.
For more information about Tay-Sachs disease carrier screening or to participate in this study, contact Amybeth Weaver, MS, CGC at irish@tay-sachs.org or call 215-887-0877. You can also go to the website and download a brochure that explains the Irish connection to Tay-Sachs.
Eight weeks after Harrison died, the Mitchells went to their first information session to help spread the word about the disease and especially to let others know that the Irish are among the most vulnerable populations. Last March, they manned a stand at the Bucks County St. Patrick’s Day Parade in Levittown (they serve on the parade committee) where they sold T-shirts, hats, and souvenirs to raise money for the parade—and passed out Tay-Sachs pamphlets for free.
“It’s important to us to raise awareness about Tay-Sachs,” says Cathy. “We need to get the word out there that it affects everybody.”
Better late than never!
Your usual trusty HTBI guide Denise Foley is enjoying a well-deserved rest, which leaves the task of filling you in on all things Irish and Philly during the upcoming holiday week up to me.
As seems to be the case every time Denise hits the road, most of the coming week is a bit on the light side. Maybe everyone’s at the shore.
But there is one big exception: Sunday.
Let’s start with the Project Children Benefit in Kildare’s in Manayunk, Sunday from noon to 3. We’ve been there, of course, and it’s a great venue in one of Philly’s funkiest neighborhoods. Hard to think of a better place for the fund-raiser. Project Children helps contribute to peace in Northern Ireland in its own small but significant way, bringing Protestant and Catholic kids from that often troubled area of the world to the United States for summer vacations. Price of admission is $20 for adults, and $10 for kids. (Kids under 10 get in for free.) There’s going to be a great buffet, plenty of draft beers to keep you cool, and Irish tuneage by Frank Daly of Jamison and friends. Irish dancers, too, of course, and fun for the kiddies, including face-painting.
Sunday being a bright, beautiful sun-filled day in the summer, there is, of course, more to do on Sunday. Starting at 2 the same day, there’s Irish football and hurling at cardinal Dougherty High School field. If you haven’t seen these uniquely Irish sports, find time sometime this summer to take in an afternoon of games. (Bring plenty of sunblock. There aren’t many trees.)
And if you love Irish music, Sunday is a day full of traditional Irish music sessions at local bars. See our calendar for all the details. It’s a pretty good bet there will be a session near you.
See you next week.